Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Centogene AG - |
RCV001809148 | SCV002059581 | uncertain significance | X-linked intellectual disability with marfanoid habitus | 2020-12-28 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003761434 | SCV004500939 | uncertain significance | FG syndrome | 2023-04-06 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 1333933). This variant has not been reported in the literature in individuals affected with MED12-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces threonine, which is neutral and polar, with serine, which is neutral and polar, at codon 1945 of the MED12 protein (p.Thr1945Ser). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) has been performed at Invitae for this missense variant, however the output from this modeling did not meet the statistical confidence thresholds required to predict the impact of this variant on MED12 protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |