Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV003596118 | SCV003268431 | benign | FG syndrome | 2023-11-07 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004632106 | SCV005133855 | uncertain significance | Familial thoracic aortic aneurysm and aortic dissection | 2024-05-23 | criteria provided, single submitter | clinical testing | The c.6159_6167delGCAGCAGCA variant (also known as p.Q2074_Q2076del) is located in coding exon 42 of the MED12 gene. This variant results from an in-frame GCAGCAGCA deletion at nucleotide positions 6159 to 6167. This results in the in-frame deletion of a at codon 2074. These amino acid positions are highly conserved in available vertebrate species. In addition, this alteration is predicted to be neutral by in silico analysis (Choi Y et al. PLoS ONE. 2012; 7(10):e46688). Based on data from gnomAD, this variant has an overall frequency of <0.01% (1/179513) total alleles studied, with 1 hemizygote(s) observed. The highest observed frequency was <0.01% (1/79541) of European (non-Finnish) alleles. Based on the available evidence, the clinical significance of this variant remains unclear. |