Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
NIHR Bioresource Rare Diseases, |
RCV000851927 | SCV000899307 | likely pathogenic | Hypofibrinogenemia | 2019-02-01 | criteria provided, single submitter | research | |
Mayo Clinic Laboratories, |
RCV001723574 | SCV005413660 | pathogenic | not provided | 2023-08-08 | criteria provided, single submitter | clinical testing | PP5, PM3_strong, PS4_moderate, PVS1 |
OMIM | RCV000017822 | SCV000038101 | pathogenic | Congenital afibrinogenemia | 2004-04-15 | no assertion criteria provided | literature only | |
Joint Genome Diagnostic Labs from Nijmegen and Maastricht, |
RCV001723574 | SCV001957791 | pathogenic | not provided | no assertion criteria provided | clinical testing | ||
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV001723574 | SCV001972555 | pathogenic | not provided | no assertion criteria provided | clinical testing | ||
ISTH- |
RCV002243650 | SCV002515723 | pathogenic | Afibrinogenemia | no assertion criteria provided | research |