Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV002287499 | SCV002578064 | pathogenic | See cases | 2022-08-26 | criteria provided, single submitter | clinical testing | ACMG categories: PVS1,PM2,PP3,PP5 |
Istanbul Faculty of Medicine, |
RCV001823201 | SCV002028347 | pathogenic | Distal arthrogryposis and CNS involvement | 2021-11-18 | no assertion criteria provided | clinical testing | Identied in three affected fetuses |
OMIM | RCV003152626 | SCV003841091 | uncertain significance | not provided | 2023-01-31 | no assertion criteria provided | literature only |