Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000654963 | SCV000776873 | likely benign | RASopathy | 2023-11-25 | criteria provided, single submitter | clinical testing | |
Genome Diagnostics Laboratory, |
RCV001813541 | SCV002060748 | uncertain significance | Noonan syndrome and Noonan-related syndrome | 2017-08-23 | criteria provided, single submitter | clinical testing | |
Genetic Services Laboratory, |
RCV001816651 | SCV002068613 | uncertain significance | not specified | 2019-02-22 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV003144457 | SCV003829285 | uncertain significance | not provided | 2019-09-03 | criteria provided, single submitter | clinical testing | |
St. |
RCV003325210 | SCV004031190 | uncertain significance | CBL-related disorder | 2023-06-20 | criteria provided, single submitter | clinical testing | The CBL c.1753C>T (p.Arg585Cys) missense change has a maximum subpopulation frequency of 0.014% in gnomAD v2.1.1 (https://gnomad.broadinstitute.org/). The in silico tool REVEL is inconclusive about a pathogenic or benign effect of this variant on protein function, and to our knowledge functional studies have not been performed. A variant affecting the same residue, p.R585L, has been reported in an individual with neonatal hypertrophic cardiomyopathy who also harbored a pathogenic variant in the PTPN11 gene (PMID: 25731833). To our knowledge, this variant has not been reported in individuals with juvenile myelomonocytic leukemia. In summary, the evidence currently available is insufficient to determine the clinical significance of this variant. It has therefore been classified as of uncertain significance. |