Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV002510642 | SCV002820138 | likely pathogenic | Megaconial type congenital muscular dystrophy | criteria provided, single submitter | clinical testing | The variant c.150C>A in CHKB (NM_005198.4) has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. Null variant (nonsense), in gene CHKB for which loss-of-function is a known mechanism of disease. The nucleotide change in CHKB is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Likely Pathogenic. |