Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV001727306 | SCV001961858 | uncertain significance | not provided | 2021-09-01 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001727306 | SCV003525631 | pathogenic | not provided | 2022-05-19 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 1298976). This premature translational stop signal has been observed in individual(s) with autism spectrum disorder (PMID: 26185613). This variant is present in population databases (rs373689624, gnomAD 0.0009%). This sequence change creates a premature translational stop signal (p.Arg4270*) in the FAT1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in FAT1 are known to be pathogenic (PMID: 30862798). |