Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003340893 | SCV004047713 | uncertain significance | Rett syndrome, congenital variant | criteria provided, single submitter | clinical testing | The missense variant c.142C>T (p.His48Tyr) in FOXG1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. The amino acid Histidine at position 48 is changed to a Tyrosine changing protein sequence and it might alter its composition and physico-chemical properties. The residue is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |