Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003829535 | SCV004628385 | uncertain significance | not provided | 2023-01-05 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). This variant has not been reported in the literature in individuals affected with NCKAP1L-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces lysine, which is basic and polar, with asparagine, which is neutral and polar, at codon 906 of the NCKAP1L protein (p.Lys906Asn). |
Neuberg Centre For Genomic Medicine, |
RCV004723506 | SCV005329416 | uncertain significance | Immunodeficiency 72 with autoinflammation | 2023-05-20 | criteria provided, single submitter | clinical testing | The observed missense variant c.2718G>C (p.Lys906Asn) in NCKAP1L gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Lys906Asn variant is present with an allele frequency of 0.0004% on gnomAD exomes database. This variant has not been submitted to the ClinVar database. Multiple lines of computational evidence (SIFT - damaging; Polyphen - probably damaging; MutationTaster - disease causing) predict a damaging effect on protein structure and function for this variant. The amino acid change p.Lys906Asn in NCKAP1L is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. The amino acid Lys at position 906 is changed to a Asn changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as a Variant of Uncertain Significance (VUS). |