Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000525377 | SCV000632806 | likely benign | Juvenile polyposis syndrome | 2024-04-24 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV003999048 | SCV004822169 | uncertain significance | Juvenile polyposis/hereditary hemorrhagic telangiectasia syndrome | 2023-11-30 | criteria provided, single submitter | clinical testing | This variant causes an A to C nucleotide substitution at the -9 position of intron 6 of the SMAD4 gene. To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with SMAD4-related disorders in the literature. This variant has been identified in 1/251390 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |