Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ISTH- |
RCV002264883 | SCV002546499 | uncertain significance | Congenital amegakaryocytic thrombocytopenia | criteria provided, single submitter | clinical testing | ||
Prevention |
RCV004534016 | SCV004117772 | uncertain significance | MPL-related disorder | 2023-04-14 | criteria provided, single submitter | clinical testing | The MPL c.131C>T variant is predicted to result in the amino acid substitution p.Thr44Ile. This variant has been reported in the compound heterozygous state in an individual with congenital amegakaryocytic thrombocytopenia (Lo et al. 2018. PubMed ID: 28859041). This variant has not been reported in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |