Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003340910 | SCV004047750 | uncertain significance | Thrombocythemia 2 | criteria provided, single submitter | clinical testing | The missense variant c.1719G>C (p.Lys573Asn) in MPL gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Lys573Asn variant is reported with allele frequency 0.0008% in gnomAD exomes and novel in 1000 Genomes. The amino acid Lys at position 573 is changed to a Asn changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Lys573Asn in MPL is predicted as conserved by PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance . |