Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genomics Laboratory, |
RCV003455870 | SCV004177040 | uncertain significance | Lymphedema-posterior choanal atresia syndrome | 2023-09-15 | criteria provided, single submitter | clinical testing | The PTPN14 c.715A>T (p.Ile239Phe) variant was identified at a near-heterozygous allelic fraction. This variant, to our knowledge, has not been reported in the medical literature. This variant is only observed on 1/152106 alleles in the general population (gnomAD v.3.1.2), indicating it is not a common variant. Computational predictors indicate that the variant is damaging; however, functional evidence that correlates with impact on PTPN14 function is lacking. Due to limited information and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |