Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Athena Diagnostics | RCV003482721 | SCV004229702 | pathogenic | not provided | 2022-11-17 | criteria provided, single submitter | clinical testing | This variant is expected to severely impact normal RNA splicing, and consequently, protein structure and/or function. This variant has been identified in at least one individual with clinical features associated with autosomal recessive Schwartz-Jampel syndrome type 1 (SJS1). This variant has not been reported in large, multi-ethnic general populations (http://gnomad.broadinstitute.org). |