Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000725837 | SCV000339833 | pathogenic | not provided | 2016-03-02 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000008497 | SCV001202873 | pathogenic | Mendelian susceptibility to mycobacterial diseases due to complete IL12RB1 deficiency | 2024-11-13 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gln32*) in the IL12RB1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in IL12RB1 are known to be pathogenic (PMID: 9603733, 12591909). This variant is present in population databases (rs121434492, gnomAD 0.02%). This premature translational stop signal has been observed in individual(s) with Mendelian susceptibility to mycobacterial disease (PMID: 9603733). ClinVar contains an entry for this variant (Variation ID: 8032). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. For these reasons, this variant has been classified as Pathogenic. |
Ce |
RCV000725837 | SCV001246165 | pathogenic | not provided | 2018-08-01 | criteria provided, single submitter | clinical testing | |
Ai |
RCV000725837 | SCV002502264 | pathogenic | not provided | 2022-03-17 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV000008497 | SCV002811763 | pathogenic | Mendelian susceptibility to mycobacterial diseases due to complete IL12RB1 deficiency | 2022-04-29 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000008497 | SCV000028705 | pathogenic | Mendelian susceptibility to mycobacterial diseases due to complete IL12RB1 deficiency | 1998-05-29 | no assertion criteria provided | literature only | |
Prevention |
RCV004755723 | SCV005345979 | pathogenic | IL12RB1-related disorder | 2024-04-13 | no assertion criteria provided | clinical testing | The IL12RB1 c.94C>T variant is predicted to result in premature protein termination (p.Gln32*). This variant was reported in three individuals with interleukin-12 receptor deficiency (de Jong et al. 1998. PubMed ID: 9603733; Fieschi C et al 2003. PubMed ID: 12591909). This variant is reported in 0.018% of alleles in individuals of European (Non-Finnish) descent in gnomAD. Nonsense variants in IL12RB1 are expected to be pathogenic. This variant is interpreted as pathogenic. |