Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Lupski Lab, |
RCV000516014 | SCV000579327 | likely pathogenic | Fibromatosis, gingival, 1 | 2017-05-01 | criteria provided, single submitter | research | This variant was identified in an individual with hereditary gingival fibromatosis. |
Labcorp Genetics |
RCV001851328 | SCV002297694 | uncertain significance | not provided | 2021-02-19 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (ExAC no frequency). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. This variant has been observed in individual(s) with gingival fibromatosis (PMID: 28686854). ClinVar contains an entry for this variant (Variation ID: 427771). This sequence change creates a premature translational stop signal (p.Asn958Serfs*9) in the REST gene. While this is not anticipated to result in nonsense mediated decay, it is expected to disrupt the last 140 amino acid(s) of the REST protein. |
OMIM | RCV000497680 | SCV000590794 | pathogenic | Fibromatosis, gingival, 5 | 2017-08-15 | no assertion criteria provided | literature only |