Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001706761 | SCV001934236 | uncertain significance | Noonan syndrome 4 | 2020-10-14 | criteria provided, single submitter | clinical testing | |
3billion | RCV001706761 | SCV002014710 | uncertain significance | Noonan syndrome 4 | 2021-10-25 | criteria provided, single submitter | clinical testing | This varant is not observed in the gnomAD v2.1.1 dataset (PM2). Missense changes are a common disease-causing mechanism (PP2). In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.885, 3Cnet: 0.980, PP3). Therefore, this variant is classified as uncertain significance according to the recommendation of ACMG/AMP guideline. |
Genome- |
RCV001706761 | SCV002763439 | uncertain significance | Noonan syndrome 4 | criteria provided, single submitter | clinical testing | ||
Genome- |
RCV002468285 | SCV002763440 | uncertain significance | Fibromatosis, gingival, 1 | criteria provided, single submitter | clinical testing |