Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000680743 | SCV000808187 | uncertain significance | not provided | 2018-04-17 | criteria provided, single submitter | clinical testing | The E9K variant in the SOS1 gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The E9K variant is not observed in large population cohorts (Lek et al., 2016). The E9K variant is a non-conservative amino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity, charge, size and/or other properties. However, in silico analyses, including protein predictors and evolutionary conservation, support that this variant does not alter protein structure/function. We interpret E9K as a variant of uncertain significance. |
Fulgent Genetics, |
RCV002493123 | SCV002789450 | uncertain significance | Fibromatosis, gingival, 1; Noonan syndrome 4 | 2021-08-17 | criteria provided, single submitter | clinical testing | |
Ce |
RCV000680743 | SCV005051505 | uncertain significance | not provided | 2024-05-01 | criteria provided, single submitter | clinical testing | SOS1: PM2 |