Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV003440177 | SCV004151426 | likely benign | not provided | 2022-10-01 | criteria provided, single submitter | clinical testing | ABCB6: BS2 |
Labcorp Genetics |
RCV003440177 | SCV004278030 | uncertain significance | not provided | 2023-06-22 | criteria provided, single submitter | clinical testing | This missense change has been observed in individual(s) with Peters' anomaly (PMID: 35170016). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant is present in population databases (rs201416447, gnomAD 0.03%). This sequence change replaces valine, which is neutral and non-polar, with phenylalanine, which is neutral and non-polar, at codon 772 of the ABCB6 protein (p.Val772Phe). |