Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genomics Laboratory, |
RCV004566496 | SCV005049530 | uncertain significance | Maffucci syndrome | 2024-02-08 | criteria provided, single submitter | clinical testing | An IDH1 c.943C>T (p.His315Tyr) variant was identified at an allelic fraction consistent with somatic origin. The variant, to our knowledge, has not been reported in the medical literature and is only observed on 4/1,461,792 alleles in the general population (gnomAD v.4.0.0), indicating it is not a common variant. Computational predictors suggest that the variant does not impact IDH1 function. Due to limited information, and based on the ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |