Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
All of Us Research Program, |
RCV004016898 | SCV004834520 | likely pathogenic | Aneurysm-osteoarthritis syndrome | 2024-01-09 | criteria provided, single submitter | clinical testing | The c.2T>C (p.Met1?) variant of the SMAD3 gene creates a start loss, resulting in a disrupted protein product. This variant has been reported in a patient with adolescent idiopathic scoliosis (PMID: 26333736). His maternal grandfather had a history of aortic aneurysm and the proband's mother, who also had this variant, had bilateral knee arthritis diagnosed at the age of forty-two years (PMID: 26333736). This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). Therefore, the c.2T>C (p.Met1?) variant of the SMAD3 gene is classified as likely pathogenic. |