Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
All of Us Research Program, |
RCV004015932 | SCV004826347 | likely pathogenic | Aneurysm-osteoarthritis syndrome | 2023-05-31 | criteria provided, single submitter | clinical testing | The c.303_304insTC (p.Glu102Serfs*15) variant of the SMAD3 gene creates an early stop codon. It is expected to result in an absent or disrupted protein product. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). Truncating variants in SMAD3 are known to be pathogenic (PMID: 21778426, 24804794). Therefore, the c.303_304insTC (p.Glu102Serfs*15) variant of the SMAD3 gene is classified as likely pathogenic. |