Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001697364 | SCV000716796 | likely benign | not provided | 2020-06-05 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001697364 | SCV002227821 | likely benign | not provided | 2025-01-19 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV002498906 | SCV002810267 | likely benign | Cataract 41; Wolfram syndrome 1; Autosomal dominant nonsyndromic hearing loss 6; Type 2 diabetes mellitus; Wolfram-like syndrome | 2021-09-22 | criteria provided, single submitter | clinical testing | |
Clinical Genomics, |
RCV003126855 | SCV003801367 | benign | Wolfram syndrome 1 | criteria provided, single submitter | research | Potent mutations in WFS1 gene are associated with Wolfram's syndrome, an autosomal recessive condition, which cause diabetes mellitus, diabetes insipidus, deafness and optic atrophy. However no sufficient evidence is found to ascertain the role of this particular variant rs150997327 in Wolfram's syndrome yet. | |
Prevention |
RCV004530761 | SCV004715953 | likely benign | WFS1-related disorder | 2023-11-21 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |