Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
UCLA Clinical Genomics Center, |
RCV000199824 | SCV000255498 | likely pathogenic | Lissencephaly due to TUBA1A mutation | 2014-05-20 | criteria provided, single submitter | clinical testing | |
Institute of Human Genetics, |
RCV000767513 | SCV000898128 | pathogenic | Tubulinopathy | 2018-07-01 | criteria provided, single submitter | literature only | A variant that is classified as pathogenic has been identified in the TUBA1A gene in a born individual of unknown sex. The c.352G>A, p.(Val118Met) variant has been reported as a variant of de novo origin. |
Gene |
RCV002225502 | SCV002504545 | pathogenic | not provided | 2024-03-19 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); Missense variants in this gene are a common cause of disease and they are underrepresented in the general population; In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 25326637, 34356170, 30744660) |
MGZ Medical Genetics Center | RCV000199824 | SCV002580174 | pathogenic | Lissencephaly due to TUBA1A mutation | 2021-09-03 | criteria provided, single submitter | clinical testing |