Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratoire de Génétique Moléculaire, |
RCV003149120 | SCV003836665 | pathogenic | Intellectual disability, autosomal dominant 14 | 2020-01-02 | criteria provided, single submitter | clinical testing | |
New York Genome Center | RCV003149120 | SCV005044118 | pathogenic | Intellectual disability, autosomal dominant 14 | 2022-06-16 | criteria provided, single submitter | clinical testing | The de novo one nucleotide deletion [c.1015del p.(Ala339LeufsTer24)] identified in exon 1 (of 20) of the ARID1A gene has not been reported in affected individuals in the literature. The variant alters the wild-type translational reading frame and is predicted to cause loss of normal protein function either through protein truncation or nonsense-mediated mRNA decay. The c.1015del variant is absent from population databases (gnomADv2, gnomADv3, TOPMed Freeze 8) suggesting it is not a common benign variant in populations represented in those databases. Based on the available evidence, the de novo c.1015del, p.(Ala339LeufsTer24) variant identified in the ARID1A gene is reported as Pathogenic. |