Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000481111 | SCV000573388 | likely pathogenic | not provided | 2017-02-17 | criteria provided, single submitter | clinical testing | The c.1920+5G>A variant in the ARID1A gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This splice site variant destroys the natural splice donor site in intron 4, which is predicted to cause abnormal gene splicing resulting in an in-frame protein product with an abnormal message. However, in the absence of RNA/functional studies, the actual effect of c.1920+5G>A in this individual is unknown. Additionally, the c.1920+5G>A variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). Therefore, we interpret c.1920+5G>A as a likely pathogenic variant |
Greenwood Genetic Center Diagnostic Laboratories, |
RCV005230950 | SCV005874102 | likely pathogenic | Intellectual disability, autosomal dominant 14 | 2024-10-28 | criteria provided, single submitter | clinical testing | PS2, PM2, PP3 |