Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Broad Center for Mendelian Genomics, |
RCV000785930 | SCV000924510 | likely pathogenic | Intellectual disability, autosomal dominant 14 | 2018-06-15 | criteria provided, single submitter | research | The heterozygous p.Trp1023Arg variant was identified by our study in one individual with Coffin-Siris syndrome. Trio exome analysis showed this variant to be de novo. This variant was absent from large population studies. The Tryptophan (Trp) at position 1023 is highly conserved in mammals and evolutionarily distant species, supporting that a change at this position may not be tolerated. In summary, although additional studies are required to fully establish its pathogenicity, this variant is likely pathogenic. |
Gene |
RCV001571164 | SCV001795584 | pathogenic | not provided | 2021-06-21 | criteria provided, single submitter | clinical testing | Not observed in large population cohorts (Lek et al., 2016); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 27535533) |