Total submissions: 2
| Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
|---|---|---|---|---|---|---|---|---|
| Ambry Genetics | RCV005382633 | SCV006049404 | uncertain significance | Inborn genetic diseases | 2025-02-13 | criteria provided, single submitter | clinical testing | The c.7270C>T (p.R2424W) alteration is located in exon 33 (coding exon 33) of the PCNT gene. This alteration results from a C to T substitution at nucleotide position 7270, causing the arginine (R) at amino acid position 2424 to be replaced by a tryptophan (W). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
| Prevention |
RCV003416981 | SCV004109042 | uncertain significance | PCNT-related disorder | 2024-06-17 | no assertion criteria provided | clinical testing | The PCNT c.7270C>T variant is predicted to result in the amino acid substitution p.Arg2424Trp. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.0056% of alleles in individuals of Latino descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |