Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002520396 | SCV001400751 | uncertain significance | Catecholaminergic polymorphic ventricular tachycardia 1 | 2021-09-02 | criteria provided, single submitter | clinical testing | This sequence change replaces proline with threonine at codon 589 of the TRDN protein (p.Pro589Thr). The proline residue is weakly conserved and there is a small physicochemical difference between proline and threonine. This variant is present in population databases (rs374035597, ExAC 0.009%). This variant has not been reported in the literature in individuals affected with TRDN-related conditions. ClinVar contains an entry for this variant (Variation ID: 355212). Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV002488789 | SCV002781048 | uncertain significance | Catecholaminergic polymorphic ventricular tachycardia 1; Catecholaminergic polymorphic ventricular tachycardia 5 | 2021-10-04 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004022015 | SCV005024119 | uncertain significance | Cardiovascular phenotype | 2024-03-11 | criteria provided, single submitter | clinical testing | The p.P589T variant (also known as c.1765C>A), located in coding exon 32 of the TRDN gene, results from a C to A substitution at nucleotide position 1765. The proline at codon 589 is replaced by threonine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this alteration remains unclear. |