Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV002267599 | SCV002549727 | uncertain significance | Torsion dystonia 4 | 2022-07-21 | criteria provided, single submitter | clinical testing | The variant c.722G>C (p.(Arg241Pro)) in exon 4 of the TUBB4A-gene is not found in the gnomAD database, it affects a highly conserved nucleotide, a highly conserved amino acid within a protein domain and there is a moderate physicochemical difference between Arg and Pro. This variant has a pathogenic computational verdict based on in silico predictions algorithms. Variant was inherited from unaffected father. ACMG criteria used for classification: PM2, PP2, PP3, BS2. |