Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Diagnostics Lab, |
RCV000258678 | SCV005187397 | likely pathogenic | Hypomyelinating leukodystrophy 6 | 2021-04-04 | criteria provided, single submitter | clinical testing | This missense variant (c.847C>A, p.Gln292Lys) has not been observed in population databases (gnomAD) but the change has been reported it the literature (PMID 25085639). Variant prediction programs suggest a deleterious effect, although no functional studies have been published. |
Gene |
RCV000258678 | SCV000328468 | not provided | Hypomyelinating leukodystrophy 6 | no assertion provided | literature only |