Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001767510 | SCV001998366 | uncertain significance | not provided | 2021-04-14 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Reported in individuals with obesity (Serra-Juhe et al., 2020); This variant is associated with the following publications: (PMID: 30926952) |
Genetic Services Laboratory, |
RCV001821984 | SCV002072064 | uncertain significance | not specified | 2017-07-12 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001767510 | SCV002486876 | benign | not provided | 2024-01-08 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002544081 | SCV003719383 | likely benign | Inborn genetic diseases | 2021-10-15 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Prevention |
RCV004746443 | SCV005363262 | uncertain significance | NTRK2-related disorder | 2024-08-14 | no assertion criteria provided | clinical testing | The NTRK2 c.746C>A variant is predicted to result in the amino acid substitution p.Ser249Tyr. This variant was reported in three individuals with early onset obesity; however, no additional information was provided to support the pathogenicity of this variant (Table S4, Serra-Juhé et al. 2019. PubMed ID: 30926952; Supplementary Table 1, Roberts KJ et al 2022. PubMed ID: 35562395). This variant is reported in 0.075% of alleles in individuals of Latino descent in gnomAD, which is more common than expected for a variant associated with autosomal dominant disease. Although we suspect that this variant may be benign, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |