Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000547513 | SCV000630635 | uncertain significance | Gastrointestinal stromal tumor | 2023-06-15 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with PDGFRA-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. ClinVar contains an entry for this variant (Variation ID: 459079). This variant is present in population databases (rs781561737, gnomAD 0.01%). This variant, c.2988_2990del, results in the deletion of 1 amino acid(s) of the PDGFRA protein (p.Glu997del), but otherwise preserves the integrity of the reading frame. |
Prevention |
RCV003409777 | SCV004114529 | uncertain significance | PDGFRA-related disorder | 2022-11-23 | criteria provided, single submitter | clinical testing | The PDGFRA c.2988_2990delGGA variant is predicted to result in an in-frame deletion (p.Glu997del). To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.0096% of alleles in individuals of Ashkenazi Jewish descent in gnomAD (http://gnomad.broadinstitute.org/variant/4-55156584-CGAG-C). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |
Gene |
RCV004760558 | SCV005369706 | uncertain significance | not provided | 2023-05-30 | criteria provided, single submitter | clinical testing | In-frame deletion of 1 amino acid in a non-repeat region; In silico analysis supports a deleterious effect on protein structure/function; Not observed at significant frequency in large population cohorts (gnomAD); Has not been previously published as pathogenic or benign to our knowledge |