Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Seattle Children's Hospital Molecular Genetics Laboratory, |
RCV002254421 | SCV002525573 | likely pathogenic | not provided | 2021-08-20 | criteria provided, single submitter | clinical testing | This variant is not reported in the medical literature, control population database (gnomAD v2.1.1) nor in ClinVar or cancer databases (cBioPortal, COSMIC, and NCI's Genomic Data Commons). This variant is a deletion of 21 base pairs predicted to result in the loss of eight amino acids and the insertion of a serine, denoted p.Trp11_Pro18delinsSer. This variant is located within the highly conserved PI3K adaptor-binding domain (ABD) region (UniProt P42336). Although this variant has not been previously reported, deletions in this region have been reported as oncogenic (PMID: 21266528, COSMIC and cBioPortal). |