Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001054980 | SCV001219344 | pathogenic | not provided | 2024-12-24 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Arg651*) in the MERTK gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in MERTK are known to be pathogenic (PMID: 24265693, 29659094). This variant is present in population databases (rs119489105, gnomAD 0.01%). This premature translational stop signal has been observed in individual(s) with clinical features of inherited retinal dystrophies (PMID: 11062461, 20300561, 25097241). ClinVar contains an entry for this variant (Variation ID: 5402). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. For these reasons, this variant has been classified as Pathogenic. |
Broad Center for Mendelian Genomics, |
RCV001723542 | SCV001950293 | pathogenic | Retinitis pigmentosa | 2021-04-01 | criteria provided, single submitter | curation | The p.Arg651Ter variant in MERTK was identified in an individual with Retinitis pigmentosa, via a collaborative study between the Broad Institute's Center for Mendelian Genomics and the Pierce lab (https://oculargenomics.meei.harvard.edu/labs/pierce-lab/lab-members/). Through a review of available evidence we were able to apply the following criteria: PVS1, PM2, PM3-P. Based on this evidence we have classified this variant as Pathogenic. If you have any questions about the classification please reach out to the Pierce Lab. |
Institute of Human Genetics, |
RCV004814840 | SCV005069116 | pathogenic | Retinal dystrophy | 2015-01-01 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000005733 | SCV000025915 | pathogenic | Retinitis pigmentosa 38 | 2010-03-09 | no assertion criteria provided | literature only | |
Faculty of Health Sciences, |
RCV001257901 | SCV001434669 | pathogenic | Autosomal recessive retinitis pigmentosa | 2018-05-23 | no assertion criteria provided | literature only |