Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV001014631 | SCV001175363 | uncertain significance | Hereditary cancer-predisposing syndrome | 2018-07-12 | criteria provided, single submitter | clinical testing | The c.216dupG variant, located in coding exon 1 of the HOXB13 gene, results from a duplication of G at nucleotide position 216, causing a translational frameshift with a predicted alternate stop codon (p.T73Dfs*54). This alteration is expected to result in premature protein truncation or nonsense-mediated mRNA decay. However, loss of function via haploinsufficiency in HOXB13 has not been clearly established as a mechanism of disease. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Laboratory of Virology, |
RCV000855936 | SCV000993927 | uncertain significance | Prostate cancer, hereditary, 1 | no assertion criteria provided | clinical testing |