Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Foundation for Research in Genetics and Endocrinology, |
RCV002463827 | SCV002600904 | uncertain significance | Autosomal recessive nonsyndromic hearing loss 48 | 2022-09-15 | criteria provided, single submitter | clinical testing | A homozygous missense variation in exon 1 of the CIB2 gene that results in the amino acid substitution of Lysine for Asparagine at codon 3 was detected . This variant has not been reported in the 1000 genomes and gnomAD databases . The in silico predictions of the variant are probably damaging by PolyPhen- 2 (HumDiv) and damaging by SIFT and LRT. The reference codon is conserved across mammals. In summary, the variant meets our criteria to be classified as a variant of uncertain significance. |