Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001765789 | SCV001999434 | pathogenic | not provided | 2024-01-29 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Prevention |
RCV004758825 | SCV005356286 | uncertain significance | PRPF8-related disorder | 2024-06-28 | no assertion criteria provided | clinical testing | The PRPF8 c.3893G>A variant is predicted to result in the amino acid substitution p.Arg1298His. To our knowledge, this variant has not been reported in the literature or in a large population database, indicating this variant is rare. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |