Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetics and Genomics Program, |
RCV004733990 | SCV005367916 | uncertain significance | Congenital long QT syndrome | no assertion criteria provided | research | The c.44G>T missense variant in SCN10A occurs in a critical domain of the gene (PM1) and is absent from population databases (PM2). In silico predictions support a damaging effect (PP3). ACMG codes: PM1, PM2, PP3. |