Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000189363 | SCV000243001 | likely pathogenic | not provided | 2024-09-17 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 27467583) |
Laboratorio de Genetica e Diagnostico Molecular, |
RCV002252036 | SCV002524030 | uncertain significance | See cases | 2019-06-14 | criteria provided, single submitter | clinical testing | ACMG classification criteria: PM1, PM2, PP3 |