Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Diagnostics Lab, |
RCV004691692 | SCV005187370 | likely pathogenic | Allan-Herndon-Dudley syndrome | 2021-01-22 | criteria provided, single submitter | clinical testing | This nonsense variant (c.394G>T, p.Glu132*) has not been observed in population databases (gnomAD) and has not been described in the literature. No functional studies have been published. It has been seen in an affected male, his sister (who is reported to be a manifesting carrier), and their mother. |