Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001592697 | SCV001823248 | pathogenic | not provided | 2024-07-23 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 36454652, 28319062, KangSR[2023]article, 31239556) |
Institute of Human Genetics, |
RCV001780414 | SCV002026296 | likely pathogenic | Intellectual disability-feeding difficulties-developmental delay-microcephaly syndrome | 2023-10-13 | criteria provided, single submitter | clinical testing | Criteria applied: PS4_MOD,PM1,PM5,PM2_SUP |
Suma Genomics | RCV001780414 | SCV002097024 | likely pathogenic | Intellectual disability-feeding difficulties-developmental delay-microcephaly syndrome | criteria provided, single submitter | clinical testing |