Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002312471 | SCV000847028 | uncertain significance | Inborn genetic diseases | 2023-11-21 | criteria provided, single submitter | clinical testing | The c.358C>T (p.P120S) alteration is located in exon 1 (coding exon 1) of the TBR1 gene. This alteration results from a C to T substitution at nucleotide position 358, causing the proline (P) at amino acid position 120 to be replaced by a serine (S). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Gene |
RCV001766574 | SCV001999689 | uncertain significance | not provided | 2022-09-08 | criteria provided, single submitter | clinical testing | Not observed in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
New York Genome Center | RCV001836874 | SCV002097762 | uncertain significance | Autism, susceptibility to, 5 | 2021-01-29 | criteria provided, single submitter | clinical testing | The c.358C>T (p.Pro120Ser) variant identified in the TBR1 gene substitutes a well conserved Proline for Serine at amino acid 120/683 (exon 1/6). This variant is absent from gnomAD(v3.1) suggesting it is not a common benign variant in the populations represented in that database. In silico algorithms predict this variant to be Tolerated (SIFT; score: 0.057) and Benign (REVEL; score:0.207) to the function of the canonical transcript. This variant is reported as a Variant of Uncertain Significance in ClinVar (VarID:587992), and to our current knowledge has not been reported in affected individuals in the literature. The p.Pro120 residue is not within a mapped domain of TBR1 (UniProtKB:Q16650). Given the lack of compelling evidence for its pathogenicity, the c.358C>T (p.Pro120Ser) variant identified in the TBR1 gene is reported as a Variant of Uncertain Significance. |
3billion, |
RCV001836874 | SCV005328547 | likely benign | Autism, susceptibility to, 5 | 2024-09-20 | criteria provided, single submitter | clinical testing | The variant was identified in at least one patient who was diagnosed with a different variant in another gene and showed no symptoms related to the gene containing the variant in question. |