Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003075287 | SCV003468778 | uncertain significance | Senior-Loken syndrome 7; Bardet-Biedl syndrome 16 | 2022-04-23 | criteria provided, single submitter | clinical testing | This sequence change replaces aspartic acid, which is acidic and polar, with asparagine, which is neutral and polar, at codon 40 of the SDCCAG8 protein (p.Asp40Asn). This variant is present in population databases (rs202114636, gnomAD 0.006%). This variant has not been reported in the literature in individuals affected with SDCCAG8-related conditions. Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The asparagine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV005266513 | SCV005931851 | uncertain significance | Inborn genetic diseases | 2024-12-25 | criteria provided, single submitter | clinical testing | The c.118G>A (p.D40N) alteration is located in exon 2 (coding exon 2) of the SDCCAG8 gene. This alteration results from a G to A substitution at nucleotide position 118, causing the aspartic acid (D) at amino acid position 40 to be replaced by an asparagine (N). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Prevention |
RCV004736261 | SCV005365534 | uncertain significance | SDCCAG8-related disorder | 2024-08-07 | no assertion criteria provided | clinical testing | The SDCCAG8 c.118G>A variant is predicted to result in the amino acid substitution p.Asp40Asn. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.0058% of alleles in individuals of Latino descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |