Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001361040 | SCV001557001 | uncertain significance | Senior-Loken syndrome 7; Bardet-Biedl syndrome 16 | 2022-06-13 | criteria provided, single submitter | clinical testing | This sequence change replaces glutamic acid, which is acidic and polar, with lysine, which is basic and polar, at codon 584 of the SDCCAG8 protein (p.Glu584Lys). This variant is present in population databases (rs150961792, gnomAD 0.02%). This variant has not been reported in the literature in individuals affected with SDCCAG8-related conditions. ClinVar contains an entry for this variant (Variation ID: 1052788). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C15"). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV001361040 | SCV002782774 | uncertain significance | Senior-Loken syndrome 7; Bardet-Biedl syndrome 16 | 2021-09-28 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004528482 | SCV004103609 | uncertain significance | SDCCAG8-related disorder | 2023-08-17 | criteria provided, single submitter | clinical testing | The SDCCAG8 c.1750G>A variant is predicted to result in the amino acid substitution p.Glu584Lys. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.020% of alleles in individuals of African descent in gnomAD (http://gnomad.broadinstitute.org/variant/1-243581275-G-A). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |