Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002625314 | SCV003521499 | uncertain significance | Senior-Loken syndrome 7; Bardet-Biedl syndrome 16 | 2022-03-23 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. This variant has not been reported in the literature in individuals affected with SDCCAG8-related conditions. This variant is present in population databases (rs368583241, gnomAD 0.0009%). This sequence change replaces threonine, which is neutral and polar, with isoleucine, which is neutral and non-polar, at codon 703 of the SDCCAG8 protein (p.Thr703Ile). |
Prevention |
RCV004529225 | SCV004106276 | uncertain significance | SDCCAG8-related disorder | 2023-06-21 | criteria provided, single submitter | clinical testing | The SDCCAG8 c.2108C>T variant is predicted to result in the amino acid substitution p.Thr703Ile. To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |