Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001839196 | SCV002099140 | uncertain significance | Floating-Harbor syndrome | 2021-03-19 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002542827 | SCV003481360 | uncertain significance | not provided | 2022-05-15 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with glutamine, which is neutral and polar, at codon 1871 of the SRCAP protein (p.Arg1871Gln). This variant is present in population databases (rs375163006, gnomAD 0.009%). This variant has not been reported in the literature in individuals affected with SRCAP-related conditions. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |