Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV003235529 | SCV003933638 | pathogenic | not provided | 2023-09-15 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation, as the last 824 amino acids are lost, and other loss-of-function variants have been reported downstream in HGMD; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 35904121, 27934915, 32615693, 35664296, 23621943, 30138938) |
Service de Génétique Moléculaire, |
RCV001270394 | SCV001450677 | pathogenic | Floating-Harbor syndrome | 2020-09-22 | no assertion criteria provided | clinical testing |