Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000579331 | SCV000681073 | pathogenic | not provided | 2019-10-12 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed in large population cohorts (Lek et al., 2016); This variant is associated with the following publications: (PMID: 30245513) |
Klinisk genetik och genomik Research, |
RCV003447148 | SCV004174843 | likely pathogenic | Autosomal dominant intellectual disability-craniofacial anomalies-cardiac defects syndrome | 2023-11-09 | criteria provided, single submitter | research | Syndromic multiple suture craniosynostosis |