Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000578941 | SCV000680534 | pathogenic | not provided | 2022-10-14 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 30245513, 25728775, 31754438, 27133397) |
Ce |
RCV000578941 | SCV001247734 | pathogenic | not provided | 2019-02-01 | criteria provided, single submitter | clinical testing | |
UCLA Clinical Genomics Center, |
RCV000167547 | SCV000196748 | pathogenic | Autosomal dominant intellectual disability-craniofacial anomalies-cardiac defects syndrome | 2015-01-15 | no assertion criteria provided | clinical testing | |
OMIM | RCV000167547 | SCV000218422 | pathogenic | Autosomal dominant intellectual disability-craniofacial anomalies-cardiac defects syndrome | 2015-03-05 | no assertion criteria provided | literature only | |
Laboratory of Molecular Genetics |
RCV000578941 | SCV000778200 | pathogenic | not provided | 2016-06-01 | no assertion criteria provided | clinical testing |